[Congenital vallecular cyst with weight disorders. Case report]. / Quiste congénito de la valécula con alteraciones del peso. Caso clínico.

Vallecula cysts are a rare condition in children, with stridor being the most common symptom and growth alterations the more uncommon. We present a 2 months-old child referred by low weight gain from birth, with a history of choking when feeding. He had no respiratory distress but struck mouth breathing and neck hyperextension with lateralization to the right. The esophagogram showed a mass displacing hypopharynx and larynx reflux of contrast into the bronchial tree. The cyst was resected by direct laryngoscopy with marsupialization technique. The outcome was favorable, without recurrence until the fourth month of monitoring.

Quiste congénito de la valécula con alteraciones del peso: Caso clínico / Congenital vallecular cyst with weight disorders: Case report

Los quistes de la valécula son un trastorno raro en los niños; el estridor es el síntoma más frecuente y la alteración del crecimiento, el más infrecuente. Se presenta el caso de un niño de 2 meses referido por la escasa ganancia ponderal desde su nacimiento, con antecedentes de atragantamiento al alimentarse. No presentaba dificultad respiratoria, pero llamaba la atención la respiración bucal y la hiperextensión del cuello con lateralización hacia la derecha. El esofagograma mostró una masa hipofaríngea que desplazaba la laringe y reflujo del medio de contraste hacia el árbol bronquial. Por laringoscopia directa se resecó un quiste con técnica de marsupialización. La evolución fue favorable, sin recidivas, hasta el cuarto mes de seguimiento.

Vallecula cysts are a rare condition in children, with stridor being the most common symptom and growth alterations the more uncommon. We present a 2 months-old child referred by low weight gain from birth, with a history of choking when feeding. He had no respiratory distress but struck mouth breathing and neck hyperextension with lateralization to the right. The esophagogram showed a mass displacing hypopharynx and larynx reflux of contrast into the bronchial tree. The cyst was resected by direct laryngoscopy with marsupialization technique. The outcome was favorable, without recurrence until the fourth month of monitoring.

Quiste congénito de la valécula con alteraciones del peso: Caso clínico / Congenital vallecular cyst with weight disorders: Case report

Los quistes de la valécula son un trastorno raro en los niños; el estridor es el síntoma más frecuente y la alteración del crecimiento, el más infrecuente. Se presenta el caso de un niño de 2 meses referido por la escasa ganancia ponderal desde su nacimiento, con antecedentes de atragantamiento al alimentarse. No presentaba dificultad respiratoria, pero llamaba la atención la respiración bucal y la hiperextensión del cuello con lateralización hacia la derecha. El esofagograma mostró una masa hipofaríngea que desplazaba la laringe y reflujo del medio de contraste hacia el árbol bronquial. Por laringoscopia directa se resecó un quiste con técnica de marsupialización. La evolución fue favorable, sin recidivas, hasta el cuarto mes de seguimiento.(AU)

Vallecula cysts are a rare condition in children, with stridor being the most common symptom and growth alterations the more uncommon. We present a 2 months-old child referred by low weight gain from birth, with a history of choking when feeding. He had no respiratory distress but struck mouth breathing and neck hyperextension with lateralization to the right. The esophagogram showed a mass displacing hypopharynx and larynx reflux of contrast into the bronchial tree. The cyst was resected by direct laryngoscopy with marsupialization technique. The outcome was favorable, without recurrence until the fourth month of monitoring.(AU)

Quiste congénito de la valécula con alteraciones del peso. Caso clínico. / [Congenital vallecular cyst with weight disorders. Case report].

Vallecula cysts are a rare condition in children, with stridor being the most common symptom and growth alterations the more uncommon. We present a 2 months-old child referred by low weight gain from birth, with a history of choking when feeding. He had no respiratory distress but struck mouth breathing and neck hyperextension with lateralization to the right. The esophagogram showed a mass displacing hypopharynx and larynx reflux of contrast into the bronchial tree. The cyst was resected by direct laryngoscopy with marsupialization technique. The outcome was favorable, without recurrence until the fourth month of monitoring.

Manifestación laríngea de linfoma no Hodgkin de células B / Laryngeal manifestation of B-cell non-Hodgkin lymphoma

Los linfomas laríngeos primarios son raros, representando menos del 1% de ellos. Los linfomas no Hodgkin (LNH) extranodales aparecen generalmente en lugares donde hay tejido linfoide como el intestino delgado o la parótida, siendo muy raros en órganos con poca o ausente cantidad de este tejido como la laringe. Cuando se encuentran en estadios avanzados, su debut laríngeo ha sido poco documentado. Presentamos el caso de un LNH linfocítico de células pequeñas en estadio IV E con primera manifestación clínica a nivel laríngeo, así como su manejo y seguimiento evolutivo(AU)

Laryngeal lymphomas are rare, involving less than 1% of all laryngeal tumours. Extranodal non-Hodgkin lymphomas generally appear in places where lymphoid tissue exists, such as the small bowel or parotid; they are very unusual in organs with little or no presence of lymphoid tissue, such as the larynx. When advanced stages are established, initial lymphoma manifestation at the laryngeal level has rarely been documented. We present a case of a small cell lymphocytic lymphoma at stage IV/E with initial laryngeal symptoms and indicate its management and follow up(AU)

Cordoma extraóseo de nasofaringe en edad pediátrica / Extraosseous chordoma of nasopharynx in paediatric age

Los cordomas intracraneales son tumores relativamente raros localmente agresivos, que probablemente se originan de remanentes embrionarios de la notocorda. La localización primaria más frecuente es el sacro, seguida en orden de frecuencia por el clivus. Cuando los cordomas de base de cráneo tienen una localización extraósea (sin destrucción lítica del hueso) mimetizan cualquier otra lesión de nasofaringe. Presentamos el caso de un cordoma extraóseo primario en edad pediátrica que se origina en la nasofaringe, con la intención de mejorar el diagnóstico y tratamiento postoperatorio de este raro tumor(AU)

Intracranial chordomas are relatively rare locally aggressive tumours that probably originate from embryonic remnants of the notochord. They typically arise from the sacrum and secondly in the skull base/clivus region. When skull base chordomas occur at an extraosseous location (without lytic bone destruction), they may mimic other lesions of the nasopharynx. We present a case of primarily extraosseous chordoma in paediatric age, involving the nasopharynx, to improve preoperative diagnosis and postoperative management of this rare tumour(AU)

Extraosseous chordoma of nasopharynx in paediatric age.

Intracranial chordomas are relatively rare locally aggressive tumours that probably originate from embryonic remnants of the notochord. They typically arise from the sacrum and secondly in the skull base/clivus region. When skull base chordomas occur at an extraosseous location (without lytic bone destruction), they may mimic other lesions of the nasopharynx. We present a case of primarily extraosseous chordoma in paediatric age, involving the nasopharynx, to improve preoperative diagnosis and postoperative management of this rare tumour.

Laryngeal manifestation of B-cell non-Hodgkin lymphoma.

Laryngeal lymphomas are rare, involving less than 1% of all laryngeal tumours. Extranodal non-Hodgkin lymphomas generally appear in places where lymphoid tissue exists, such as the small bowel or parotid; they are very unusual in organs with little or no presence of lymphoid tissue, such as the larynx. When advanced stages are established, initial lymphoma manifestation at the laryngeal level has rarely been documented. We present a case of a small cell lymphocytic lymphoma at stage IV/E with initial laryngeal symptoms and indicate its management and follow up.

Papilomas invertidos nasosinusales. Revisión de 10 años / Sinunasal inverted papilloma. A 10 year review

Objetivos. Analizar nuestra experiencia en el diagnostico y tratamiento del papiloma invertido (PI), especialmente en relación a recientes cambios y estrategias en los abordajes quirúrgicos. Material y método. Se realizó un estudio retrospectivo durante 10 años en pacientes diagnosticados de PI consecutivamente seleccionados. El tiempo medio de seguimiento fue de 36 meses. Resultados. 15 casos diagnosticados por estudio anatomopatológico predominantemente hombres, y en estadio T2 según la clasificación Krouse. La localización primaria más común fue el seno etmoidal y maxilar. La tasa de recidiva del total de pacientes fue de 40%, con predominio de los pacientes sometidos a abordaje mixto (abierto y endoscópico). Conclusiones. La modalidad de tratamiento depende de la localización y extensión de la enfermedad. Se recomienda un seguimiento anual endoscópico para valorar los resultados del tratamiento y, de por vida debido a posibles recurrencias tardías(AU)

Aim. To analyze our experience in the diagnostic and treatment of inverted papilloma (IP), especially based on recent changes and strategies through surgical approach. Material and method. This is a retrospective chart study over a 10-year period in patients with IP consecutively selected. The mean follow-up period was 36 month. Material and method. This is a retrospective chart study over a 10-year period in patients with IP consecutively selected. The mean follow-up period was 36 month. Results. 15 cases diagnosed by anatomopathological study predominantly males, and T2 stage according to Krouseìs classification system. Most common primary localization of the tumor was ethmoid and maxillary sinus. The recurrence rate was 40%, predominantly in patients with combined approach (external and endoscopic). Results. 15 cases diagnosed by anatomopathological study predominantly males, and T2 stage according to Krouseìs classification system. Most common primary localization of the tumor was ethmoid and maxillary sinus. The recurrence rate was 40%, predominantly in patients with combined approach (external and endoscopic). Conclusions. To analyze our experience in the diagnostic and treatment of inverted papilloma (IP), especially based on recent changes and strategies through surgical approach. The treatment modality is related to the location and extent of the disease. Annual endoscopic follow-up observation is recommended for the preliminary report on the treatment results of this condition and, lifelong follow-up for possible late recurrences. Conclusions. The treatment modality is related to the location and extent of the disease. Annual endoscopic follow-up observation is recommended for the preliminary report on the treatment results of this condition and, lifelong follow-up for possible late recurrences(AU)